E.V. Zasim, V.V. Strogiy
This review presents current data on the causes, pathogenesis of development from the standpoint of electrophysiology of the cardiac conduction system of the WPW syndrome, and also discusses the methods of diagnosis and treatment of this syndrome in childhood. Particular attention is paid to the role of anatomical and physiological features, the development of the autonomic nervous system and the formation of the cardiac conduction system in children. The role of connective tissue dysplasia and the presence of an inflammatory process in the cardiac system are considered among the possible causes of WPW syndrome today. A comparative characteristic of antiarrhythmic therapy in children for the prevention of tachycardia attacks is provided, and some indications for radiofrequency ablation and its effectiveness in children with this pathology are presented.
keywords: WPW syndrome, WPW phenomenon, children, radiofrequency ablation, paroxysmal tachycardia

for references: E.V. Zasim, V.V. Strogiy. WPW syndrome in childhood: unsolved problems. Neotlozhnaya kardiologiya i kardioovaskulyarnye riski [Emergency cardiology and cardiovascular risks], 2019, vol. 3, no. 1, pp. 462–473

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